While dermatofibrosarcoma protuberans most commonly involves the trunk, extremities, scalp, and neck, occasional cases located in the face.
Dermatofibrosarcoma protuberans (DFSP) is a rare type of malignant tumor that occurs in the dermis, the second layer of the skin. Although metastasis rarely occurs, DFSP is a locally aggressive tumor with a high recurrence rate. It usually presents in early or middle adult life between 20 and 50 years of age, but all ages can be affected. The tumour is rare in children. Dermatofibrosarcoma protuberans usually presents as a large indurated plaque several centimeters in diameter. It is composed of firm, irregular nodules varying in color from flesh to reddish brown. Males are affected slightly more frequently than females. There does not appear to be any racial predilection. It is locally aggressive and highly recurrent malignant neoplasm.
